- CASE FILE
I was found to have Arterial Fibromuscular Dysplasia incidentally, and Arterial Pulmonary Sarcoma-trying to find the relationship
ABOUT THIS CASE FILE
I have a medical history of carotid bruits, migraine with aura, heart murmur, pulmonary artery sarcoma, arterial Fibromuscular Dysplasia, Factor V, asthma, atrial fibrillation and pulmonary arterial stenosis/occlusion. The FMD and pulmonary growth were found incidentally as I was asymptomatic and only found after carotid bruits were investigated. My heart is normal, and so is my right lung leading the doctors to believe this may be a chronic condition. The doctors also speculate my atrial fibrillation was triggered by the growth in my pulmonary artery. I started with afib nearly 6 years ago, so the growth has been there for quite some time according to their logic. My heart murmur has become less pronounced after having surgery to remove part of the pulmonary artery growth for biopsy leading my lung doctor to believe it is the growth creating the turbulent sound in my artery. The doctors speculate they are hearing the turbulence from the pulmonary artery, not the heart murmur, again meaning this has been there quite a while since I have had a "heart murmur" since childhood. The doctors are curious to the connection of all of my symptoms to my newly diagnosed FMD. I have had chemotherapy to shrink the "growth" in my pulmonary artery and due for surgery to remove partial or all of left lung due to total occlusion of lung from probable FMD in the pulmonary artery creating dead tissue in the lung. Also surgical repair/replacement of occluded pulmonary arteries. The first surgery I had the doctor was a bit taken back and not sure of what he witnessed. He mentioned "fibrous" tissue in the pulmonary artery which made me wonder about FMD, and not the pathology of pulmonary sarcoma from the biopsy taken. I am on just a baby aspirin for my Factor V, afib and FMD; also on afib medication. I am left now knowing exactly what we are dealing with here, I have been to numerous doctors and feel I have a team currently taking this all very seriously. I also feel they are not entirely clear on what they are dealing with either, however. I am pain free, but the anxiety of having the doctors being so unsure as to how to proceed is unnerving.